Arrhythmogenic right ventricular cardiomyopathy/dysplasia

Julia H. Indik, Frank I. Marcus

Research output: Contribution to journalReview article

7 Scopus citations

Abstract

Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is characterized by the patchy replacement of myocardium by fatty or fibrofatty tissue. These changes lead to structural abnormalities including right ventricular enlargement and wall motion abnormalities that can be detected by echocardiography, angiography, and cine MRI. ARVC/D is a genetically heterogeneous disorder, since it has been linked to several chromosomal loci. Myocarditis may also be a contributing etiological factor. Patients are typically diagnosed during adolescence or young adulthood. Presenting symptoms are generally related to ventricular arrhythmias. Concern for the risk of sudden cardiac death may lead to the implantation of an intracardiac defibrillator. An ongoing multicenter international registry should further our understanding of this disease.

Original languageEnglish (US)
Pages (from-to)148-156
Number of pages9
JournalIndian Pacing and Electrophysiology Journal
Volume3
Issue number3
StatePublished - Jul 1 2003

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Physiology (medical)

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