Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is characterized by regional or global abnormalities of right ventricular (RV) structure and function and ventricular tachyarrhythmias including sudden death [1, 2]. It is an inheritable cardiomyopathy predominantly affecting the myocardium of the RV free wall. Progressive atrophy and loss of myocytes with subsequent fatty and/or fibrous tissue replacement and interspersed surviving myocyte fibers provide the morphological substrate for re-entrant arrhythmias and regional (segmental) or global (diffuse) abnormalities of RV structure and function. In the advanced stages of ARVC/D, clinical signs of right or global heart failure and left ventricular (LV) involvement may develop .
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