Intravascular lymphomatosis (malignant angioendotheliomatosis) presenting as pulmonary hypertension

Linda S Snyder, K. R. Harmon, R. D. Estensen

Research output: Contribution to journalArticle

46 Scopus citations


Intravascular lymphomatosis is a rare lymphoma characterized by proliferation of malignant cells within the lumen of small blood vessels. We describe a case of intravascular lymphomatosis resulting in pulmonary hypertension, hypoxemia, and dyspnea. This lymphoma occasionally responds to combination chemotherapy, suggesting that pulmonary hypertension secondary to intravascular lymphomatosis may be reversible. Intravascular lymphomatosis should be considered in the differential diagnosis of pulmonary hypertension.

Original languageEnglish (US)
Pages (from-to)1199-1200
Number of pages2
Issue number5
Publication statusPublished - 1989
Externally publishedYes


ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine

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