In a series of ten patients with the WeillMarchesani syndrome, ectopia lentis occurred in 14 of 19 eyes. Glaucoma was found in 13 of the 17 eyes tested; surgical intervention in seven cases resulted in intraocular pressure control in six, although two of these required medical therapy. Nine eyes already had glaucomatous disk and field changes when first evaluated. Earlier diagnosis and surgical treatment are necessary to improve the usually poor visual prognosis in this disorder.
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