Total artificial heart implantation in a young Marfan syndrome patient

Prashant Rao, Jack B. Keenan, Taufiek K. Rajab, Samuel S Kim, Richard Smith, Orazio Amabile, Zain I Khalpey

Research output: Contribution to journalArticle

1 Citation (Scopus)

Abstract

Introduction: Cardiovascular complications represent the leading cause of morbidity and mortality in patients with Marfan syndrome. Here, we describe a unique case where a total artificial heart was implanted in a young Marfan syndrome woman. Methods: A 22-year-old postpartum African American female with Marfan syndrome developed multiple severe valve dysfunction and biventricular failure that was refractory to medical management. She previously had a Bentall procedure for Type A aortic dissection and repair of a Type B dissection. Results: We implanted a total artificial heart with a good outcome. Conclusion: Total artificial heart is a durable option for severe biventricular failure and multiple valvular dysfunction as a bridge to transplant in a young patient with Marfan syndrome.

Original languageEnglish (US)
JournalInternational Journal of Artificial Organs
DOIs
StateAccepted/In press - Feb 1 2018

Fingerprint

Artificial heart
Artificial Heart
Marfan Syndrome
Dissection
Transplants
Refractory materials
Repair
African Americans
Postpartum Period
Morbidity
Mortality
Young Syndrome

Keywords

  • bridge to transplant
  • Marfan syndrome
  • Total artificial heart

ASJC Scopus subject areas

  • Bioengineering
  • Medicine (miscellaneous)
  • Biomaterials
  • Biomedical Engineering

Cite this

Total artificial heart implantation in a young Marfan syndrome patient. / Rao, Prashant; Keenan, Jack B.; Rajab, Taufiek K.; Kim, Samuel S; Smith, Richard; Amabile, Orazio; Khalpey, Zain I.

In: International Journal of Artificial Organs, 01.02.2018.

Research output: Contribution to journalArticle

Rao, Prashant ; Keenan, Jack B. ; Rajab, Taufiek K. ; Kim, Samuel S ; Smith, Richard ; Amabile, Orazio ; Khalpey, Zain I. / Total artificial heart implantation in a young Marfan syndrome patient. In: International Journal of Artificial Organs. 2018.
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