Vanishing bronchus intermedius syndrome in a pediatric patient with cystic fibrosis after lung transplantation

Don Hayes, Heidi M. Mansour

Research output: Contribution to journalArticle

8 Scopus citations

Abstract

Airway complications occur frequently after lung transplantation. Bronchial stenosis is the most frequently encountered complication with the most severe form of that being the vanishing bronchus intermedius syndrome (VBIS). This rare disorder has never been reported in the pediatric population. This is the first report of VBIS in a pediatric patient, specifically a 16-yr-old male patient with cystic fibrosis whose course was complicated by a lower airway infection with Aspergillus fumigatus. The VBIS responded to bronchoscopic balloon dilation and placement of an airway stent.

Original languageEnglish (US)
Pages (from-to)E333-E337
JournalPediatric transplantation
Volume16
Issue number8
DOIs
StatePublished - Dec 1 2012
Externally publishedYes

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Keywords

  • Aspergillus fumigatus
  • cystic fibrosis
  • lung transplantation
  • vanishing bronchus intermedius syndrome

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Transplantation

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